Spontaneous Brachial Pseudo-aneurysm in a 12-year-old with Kyphoscoliosis-type Ehlers-Danlos Syndrome


Gok E., Goksel O. S. , Alpagut U. , Dayioglu E.

EUROPEAN JOURNAL OF VASCULAR AND ENDOVASCULAR SURGERY, vol.44, no.5, pp.482-484, 2012 (Journal Indexed in SCI) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 44 Issue: 5
  • Publication Date: 2012
  • Doi Number: 10.1016/j.ejvs.2012.08.004
  • Title of Journal : EUROPEAN JOURNAL OF VASCULAR AND ENDOVASCULAR SURGERY
  • Page Numbers: pp.482-484

Abstract

The Ehlers-Danlos Syndrome (EDS) is a rare connective tissue disorder characterised by fragility of the soft connective tissues and widespread manifestations in skin, ligaments, joints, blood vessels and internal organs. We report a case of a 12-year-old boy, previously diagnosed with kyphoscoliosis-type EDS (type VI), presenting with a left brachial artery pseudo-aneursym with history of multiple spontaneous and post-traumatic arterial ruptures. Surgical management of this patient was performed successfully by primary repair of brachial artery lesion. (c) 2012 European Society for Vascular Surgery. Published by Elsevier Ltd. All rights reserved.