Early feeding practices in infants with phenylketonuria across Europe

Pinto, A.; Adams, S.; Ahring, K.; Allen, H.; Almeida, M.; Garcia-Arenas, D.; Arslan, N.; Assoun, M.; Altinok, Y.; Barrio-Carreras, D.; Belanger Quintana, A.; Bernabei, S.; Bontemps, C.; Boyle, F.; Bruni, G.; Bueno-Delgado, M.; Caine, G.; Carvalho, R.; Chrobot, A.; Chyz, K.; Cochrane, B.; Correia, C.; Corthouts, K.; Daly, A.; De Leo, S.; Desloovere, A.; De Meyer, A.; De Theux, A.; Didycz, B.; Dijsselhof, M.; Dokoupil, K.; Drabik, J.; Dunlop, C.; Eberle-Pelloth, W.; Eftring, K.; Ekengren, J.; Errekalde, I.; Evans, S.; Foucart, A.; Fokkema, L.; Francois, L.; French, M.; Forssell, E.; Gingell, C.; Goncalves, C.; Ozel, H.; Grimsley, A.; Gugelmo, G.; Gyure, E.; Heller, C.; Hensler, R.; Jardim, I.; Joost, C.; Joerg-Streller, M.; Jouault, C.; Jung, A.; Kanthe, M.; Koc, N.; Kok, I.; Kozanoglu, T.; Kumru, B.; Lang, F.; Lang, K.; Liegeois, I.; Liguori, A.; Lilje, R.; Lubina, O.; Manta-Vogli, P.; Mayr, D.; Meneses, C.; Newby, C.; Meyer, U.; Mexia, S.; Nicol, C.; Och, U.; Olivas, S.; Pedron-Giner, C.; Pereira, R.; Plutowska-Hoffmann, K.; Purves, J.; Dionigi, A.; Reinson, K.; Robert, M.; Robertson, L.; Rocha, J.; Rohde, C.; Rosenbaum-Fabian, S.; Rossi, A.; Ruiz, M.; Saligova, J.; Gutierrez-Sanchez, A.; Schlune, A.; Schulpis, K.; Serrano-Nieto, J.; Skarpalezou, A.; Skeath, R.; Slabbert, A.; Straczek, K.; Gizewska, M.; Terry, A.; Thom, R.; Tooke, A.; Tuokkola, J.; van Dam, E.; van den Hurk, T.; van der Ploeg, E.; Vande Kerckhove, K.; Van Driessche, M.; van Wegberg, A.; van Wyk, K.; Vasconcelos, C.; Velez Garcia, V.; Wildgoose, J.; Winkler, T.; Zolkowska, J.; Zuvadelli, J.; MacDonald, A.

doi:10.1016/j.ymgmr.2018.07.008

Early feeding practices in infants with phenylketonuria across Europe

Pinto A., Adams S., Ahring K., Allen H., Almeida M. F., Garcia-Arenas D., ...More

MOLECULAR GENETICS AND METABOLISM REPORTS, vol.16, pp.82-89, 2018 (SCI-Expanded, Scopus)

Publication Type: Article / Article
Volume: 16
Publication Date: 2018
Doi Number: 10.1016/j.ymgmr.2018.07.008
Journal Name: MOLECULAR GENETICS AND METABOLISM REPORTS
Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
Page Numbers: pp.82-89
Istanbul University Affiliated: Yes

Abstract

Background: In infants with phenylketonuria (PKU), dietary management is based on lowering and titrating phenylalanine (Phe) intake from breast milk or standard infant formula in combination with a Phe-free infant formula in order to maintain blood Phe levels within target range. Professionals use different methods to feed infants with PKU and our survey aimed to document practices across Europe.