Early feeding practices in infants with phenylketonuria across Europe

Pinto, A.; Adams, S.; Ahring, K.; Allen, H.; Almeida, M.; Garcia-Arenas, D.; Arslan, N.; Assoun, M.; Altinok, Y.; Barrio-Carreras, D.; Belanger Quintana, A.; Bernabei, S.; Bontemps, C.; Boyle, F.; Bruni, G.; Bueno-Delgado, M.; Caine, G.; Carvalho, R.; Chrobot, A.; Chyz, K.; Cochrane, B.; Correia, C.; Corthouts, K.; Daly, A.; De Leo, S.; Desloovere, A.; De Meyer, A.; De Theux, A.; Didycz, B.; Dijsselhof, M.; Dokoupil, K.; Drabik, J.; Dunlop, C.; Eberle-Pelloth, W.; Eftring, K.; Ekengren, J.; Errekalde, I.; Evans, S.; Foucart, A.; Fokkema, L.; Francois, L.; French, M.; Forssell, E.; Gingell, C.; Goncalves, C.; Ozel, H.; Grimsley, A.; Gugelmo, G.; Gyure, E.; Heller, C.; Hensler, R.; Jardim, I.; Joost, C.; Joerg-Streller, M.; Jouault, C.; Jung, A.; Kanthe, M.; Koc, N.; Kok, I.; Kozanoglu, T.; Kumru, B.; Lang, F.; Lang, K.; Liegeois, I.; Liguori, A.; Lilje, R.; Lubina, O.; Manta-Vogli, P.; Mayr, D.; Meneses, C.; Newby, C.; Meyer, U.; Mexia, S.; Nicol, C.; Och, U.; Olivas, S.; Pedron-Giner, C.; Pereira, R.; Plutowska-Hoffmann, K.; Purves, J.; Dionigi, A.; Reinson, K.; Robert, M.; Robertson, L.; Rocha, J.; Rohde, C.; Rosenbaum-Fabian, S.; Rossi, A.; Ruiz, M.; Saligova, J.; Gutierrez-Sanchez, A.; Schlune, A.; Schulpis, K.; Serrano-Nieto, J.; Skarpalezou, A.; Skeath, R.; Slabbert, A.; Straczek, K.; Gizewska, M.; Terry, A.; Thom, R.; Tooke, A.; Tuokkola, J.; van Dam, E.; van den Hurk, T.; van der Ploeg, E.; Vande Kerckhove, K.; Van Driessche, M.; van Wegberg, A.; van Wyk, K.; Vasconcelos, C.; Velez Garcia, V.; Wildgoose, J.; Winkler, T.; Zolkowska, J.; Zuvadelli, J.; MacDonald, A.

doi:10.1016/j.ymgmr.2018.07.008

Early feeding practices in infants with phenylketonuria across Europe

Atıf İçin Kopyala

Pinto A., Adams S., Ahring K., Allen H., Almeida M. F., Garcia-Arenas D., ...Daha Fazla

MOLECULAR GENETICS AND METABOLISM REPORTS, cilt.16, ss.82-89, 2018 (SCI-Expanded)

Yayın Türü: Makale / Tam Makale
Cilt numarası: 16
Basım Tarihi: 2018
Doi Numarası: 10.1016/j.ymgmr.2018.07.008
Dergi Adı: MOLECULAR GENETICS AND METABOLISM REPORTS
Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
Sayfa Sayıları: ss.82-89
İstanbul Üniversitesi Adresli: Evet

Özet

Background: In infants with phenylketonuria (PKU), dietary management is based on lowering and titrating phenylalanine (Phe) intake from breast milk or standard infant formula in combination with a Phe-free infant formula in order to maintain blood Phe levels within target range. Professionals use different methods to feed infants with PKU and our survey aimed to document practices across Europe.