Clinical, Genetic, and Outcome Characteristics of Pediatric Patients with Primary Hemophagocytic Lymphohistiocytosis

Nepesov S., Yaman Y., Elli M., Bayram N., Ozdilli K., Kiykim A., ...Daha Fazla

TURKISH ARCHIVES OF PEDIATRICS, cilt.57, sa.4, ss.398-405, 2022 (ESCI) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 57 Sayı: 4
  • Basım Tarihi: 2022
  • Doi Numarası: 10.5152/turkarchpediatr.2022.21314
  • Dergi Adı: TURKISH ARCHIVES OF PEDIATRICS
  • Derginin Tarandığı İndeksler: Emerging Sources Citation Index (ESCI), Scopus, TR DİZİN (ULAKBİM)
  • Sayfa Sayıları: ss.398-405
  • Anahtar Kelimeler: Genetic analysis, children, primary hemophagocytic lymphohistiocytosis, NERVOUS-SYSTEM INVOLVEMENT, CNS INVOLVEMENT, CHILDREN, FREQUENCY, ADULTS, HLH
  • İstanbul Üniversitesi Adresli: Evet

Özet

ObjectIive: In this study, we sought to describe the clinical, laboratory, and genetic characteristics of patients diagnosed with primary hemophagocytic lymphohistiocytosis. Thus, we aimed to evaluate the early diagnosis and appropriate treatment options for pediatric hemophagocytic lymphohistiocytosis patients.