Secondary pulmonary arterial hypertension in a patient with common variable immunodeficiency: Treatment with low dose sildenafil
Anatolian Journal of Clinical Investigation, cilt.3, sa.1, ss.97-99, 2009 (Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 3 Sayı: 1
- Basım Tarihi: 2009
- Dergi Adı: Anatolian Journal of Clinical Investigation
- Derginin Tarandığı İndeksler: Scopus
- Sayfa Sayıları: ss.97-99
- İstanbul Üniversitesi Adresli: Hayır
Özet
The present report describes a patient with common variable immunodeficiency who suffered severe pulmonary arterial hypertension and bilateral lung destruction due to bronchiectasis. Initially, the patient's treatment included antibiotics, diuretics, bronchodilators, mucolytics, oxygen and immunoglobulin replacement therapy. However, the patient's condition improved significantly only after low dose sildenafil treatment. To our best notice, our patient is the first report displaying a favorable outcome with sildenafil treatment in secondary pulmonary hypertension.