Diffuse thoracic lymphangiomatosis with disseminated intravascular coagulation in a child

Tamay Z. Ü., SARIBEYOGLU E., ONES U., ANAK S. S., GULER N., BILGIC B., ...Daha Fazla

JOURNAL OF PEDIATRIC HEMATOLOGY ONCOLOGY, cilt.27, sa.12, ss.685-687, 2005 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 27 Sayı: 12
  • Basım Tarihi: 2005
  • Doi Numarası: 10.1097/01.mph.0000193476.14493.06
  • Dergi Adı: JOURNAL OF PEDIATRIC HEMATOLOGY ONCOLOGY
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.685-687
  • Anahtar Kelimeler: disseminated intravascular coagulation, lymphangiomatosis, pediatrics, thoracic, PULMONARY LYMPHANGIOMATOSIS, CONSUMPTIVE COAGULOPATHY, MASSIVE CHYLOTHORAX, CHYLOPERICARDIUM, MEDIASTINUM
  • İstanbul Üniversitesi Adresli: Evet

Özet

An 8.5-year-old girl who presented with chronic cough and hemoptysis underwent a CT scan of the chest showing diffuse mediastinal and parenchymal infiltration and pleural effusion, and laboratory findings showed disseminated intravascular coagulation. Disseminated lymphangiomatosis was diagnosed after an open-lung biopsy. She was treated by systemic steroids, interferon, tamoxifen, chemotherapy, and radiation but died of respiratory failure and disseminated intravascular coagulation 2 years after the diagnosis. This patient represents a rare presentation of diffuse pulmonary lymphangiomatosis together with disseminated intravascular coagulation, involving both the mediastinum and pulmonary parenchyma, in a child.