Spontaneous Brachial Pseudo-aneurysm in a 12-year-old with Kyphoscoliosis-type Ehlers-Danlos Syndrome

Gok, E.; Goksel, O.; Alpagut, İbrahim; Dayioglu, E.

doi:10.1016/j.ejvs.2012.08.004

Spontaneous Brachial Pseudo-aneurysm in a 12-year-old with Kyphoscoliosis-type Ehlers-Danlos Syndrome

Atıf İçin Kopyala

Gok E., Goksel O. S., Alpagut U., Dayioglu E.

EUROPEAN JOURNAL OF VASCULAR AND ENDOVASCULAR SURGERY, cilt.44, sa.5, ss.482-484, 2012 (SCI-Expanded)

Yayın Türü: Makale / Tam Makale
Cilt numarası: 44 Sayı: 5
Basım Tarihi: 2012
Doi Numarası: 10.1016/j.ejvs.2012.08.004
Dergi Adı: EUROPEAN JOURNAL OF VASCULAR AND ENDOVASCULAR SURGERY
Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
Sayfa Sayıları: ss.482-484
İstanbul Üniversitesi Adresli: Evet

Özet

The Ehlers-Danlos Syndrome (EDS) is a rare connective tissue disorder characterised by fragility of the soft connective tissues and widespread manifestations in skin, ligaments, joints, blood vessels and internal organs. We report a case of a 12-year-old boy, previously diagnosed with kyphoscoliosis-type EDS (type VI), presenting with a left brachial artery pseudo-aneursym with history of multiple spontaneous and post-traumatic arterial ruptures. Surgical management of this patient was performed successfully by primary repair of brachial artery lesion. (c) 2012 European Society for Vascular Surgery. Published by Elsevier Ltd. All rights reserved.