Caroli's disease in children: Is it commonly misdiagnosed?

Senyuz O., Yesildag E., Kuruoglu S., Yeker Y., Emir H.

ACTA PAEDIATRICA, vol.94, no.1, pp.117-120, 2005 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Editorial Material
  • Volume: 94 Issue: 1
  • Publication Date: 2005
  • Doi Number: 10.1080/08035250410031747
  • Journal Name: ACTA PAEDIATRICA
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.117-120
  • Istanbul University Affiliated: No


Aim: Caroli's disease is a simple form of intrahepatic bile duct ectasia. It can be complicated with the involvement of liver parenchyma and portal hypertension. Herein, the difficult management of delayed presentation of Caroli's disease is reported. Methods and results: We report on four different forms of clinical presentation of Caroli's disease: an infant with fulminant liver failure, a teenager with persistent biliary fistula, a boy with hypersplenism in the face of portal hypertension and a girl with variceal bleeding.