Caroli's disease in children: Is it commonly misdiagnosed?


Senyuz O., Yesildag E., Kuruoglu S., Yeker Y., Emir H.

ACTA PAEDIATRICA, cilt.94, ss.117-120, 2005 (SCI İndekslerine Giren Dergi) identifier identifier identifier

  • Cilt numarası: 94 Konu: 1
  • Basım Tarihi: 2005
  • Doi Numarası: 10.1080/08035250410031747
  • Dergi Adı: ACTA PAEDIATRICA
  • Sayfa Sayıları: ss.117-120

Özet

Aim: Caroli's disease is a simple form of intrahepatic bile duct ectasia. It can be complicated with the involvement of liver parenchyma and portal hypertension. Herein, the difficult management of delayed presentation of Caroli's disease is reported. Methods and results: We report on four different forms of clinical presentation of Caroli's disease: an infant with fulminant liver failure, a teenager with persistent biliary fistula, a boy with hypersplenism in the face of portal hypertension and a girl with variceal bleeding.