Hereditary sensory and autonomic neuropathy: review and a case report with dental implications

Erdem T., Ozcan I. , Ilguy D., Sirin S.

JOURNAL OF ORAL REHABILITATION, cilt.27, ss.179-182, 2000 (SCI İndekslerine Giren Dergi) identifier identifier identifier

  • Cilt numarası: 27 Konu: 2
  • Basım Tarihi: 2000
  • Doi Numarası: 10.1046/j.1365-2842.2000.00474.x
  • Sayfa Sayıları: ss.179-182


Hereditary sensory and autonomic neuropathy (HSAN) is a rare syndrome which is seen in early childhood. Five different types are described. Absence of pain and self-mutilation are characteristic findings of this syndrome. Teeth in the oral cavity can cause damage to the oral tissues and tongue. When it is diagnosed, there should be co-operation between dentist and neurologist. Using an oral shield prevents the biting and, thus, traumatization of the tissues can be prevented. A case report which is diagnosed as HSAN type 4 is presented and information submitted about its treatment.