The exact nature of amyloid-like hyaline material deposits in the skin is not well understood in some disorders. Three of those - ligneous conjunctivitis, ligneous periodontitis and colloid milium - have been rarely reported in a same patient. We report a case of mucosal and skin deposits of an amyloid-like homogeneous material associated with non-Hodgkin's lymphoma and congenital auricular hypoplasia. We discussed and reviewed the literature on these unique associations to determine whether these are the same pathological process. We also noted whether this case represents a new syndrome or a coincidental association.