Being ambulatory does not secure respiratory functions of Duchenne patients.
Annals of Indian Academy of Neurology, cilt.14, sa.3, ss.182-4, 2011 (SCI-Expanded, Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 14 Sayı: 3
- Basım Tarihi: 2011
- Doi Numarası: 10.4103/0972-2327.85889
- Dergi Adı: Annals of Indian Academy of Neurology
- Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
- Sayfa Sayıları: ss.182-4
- Anahtar Kelimeler: Duchenne muscular dystrophy, north star ambulatory assessment, respiratory functions, MUSCULAR-DYSTROPHY, PULMONARY-FUNCTION
- İstanbul Üniversitesi Adresli: Evet
Özet
Aim: The aim of this work was to assess the respiratory functions of ambulatory Duchenne patients and to propose an earlier time period for intervention. Materials and Methods: Lung functions and North Star Ambulatory Assessment (NSAA) scores of Duchenne patients were evaluated simultaneously. Results: Thirty ambulatory Duchenne patients were included in this study. NSAA scores of the patients were directly correlated with arm abduction, arm adduction, and shoulder flexion strengths. Forced expiratory volume in 1 second percent predicted and forced vital capacity (FVC) percent predicted correlated inversely to age and to the NSAA score. Twelve of 13 patients with FVC values lower than 80% of predicted had NSAA scores below 24 points. None of the patients who were younger than 7 years had FVC values lower than 80% of predicted. Conclusion: Annual spirometry is necessary for Duchenne patients older than 6 years regardless of the ambulatory status.