Being ambulatory does not secure respiratory functions of Duchenne patients.

Ekici B., Ergul Y., Tatli B., Bilir F., Binboga F., Suleyman A., ...Daha Fazla

Annals of Indian Academy of Neurology, cilt.14, sa.3, ss.182-4, 2011 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 14 Sayı: 3
  • Basım Tarihi: 2011
  • Doi Numarası: 10.4103/0972-2327.85889
  • Dergi Adı: Annals of Indian Academy of Neurology
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.182-4
  • Anahtar Kelimeler: Duchenne muscular dystrophy, north star ambulatory assessment, respiratory functions, MUSCULAR-DYSTROPHY, PULMONARY-FUNCTION
  • İstanbul Üniversitesi Adresli: Evet

Özet

Aim: The aim of this work was to assess the respiratory functions of ambulatory Duchenne patients and to propose an earlier time period for intervention. Materials and Methods: Lung functions and North Star Ambulatory Assessment (NSAA) scores of Duchenne patients were evaluated simultaneously. Results: Thirty ambulatory Duchenne patients were included in this study. NSAA scores of the patients were directly correlated with arm abduction, arm adduction, and shoulder flexion strengths. Forced expiratory volume in 1 second percent predicted and forced vital capacity (FVC) percent predicted correlated inversely to age and to the NSAA score. Twelve of 13 patients with FVC values lower than 80% of predicted had NSAA scores below 24 points. None of the patients who were younger than 7 years had FVC values lower than 80% of predicted. Conclusion: Annual spirometry is necessary for Duchenne patients older than 6 years regardless of the ambulatory status.