Classification criteria for autoinflammatory recurrent fevers


GATTORNO M., Hofer M., FEDERICI S., VANONI F., BOVIS F., AKSENTIJEVICH I., ...More

ANNALS OF THE RHEUMATIC DISEASES, vol.78, no.8, pp.1025-1032, 2019 (Peer-Reviewed Journal) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 78 Issue: 8
  • Publication Date: 2019
  • Doi Number: 10.1136/annrheumdis-2019-215048
  • Journal Name: ANNALS OF THE RHEUMATIC DISEASES
  • Journal Indexes: Science Citation Index Expanded, Scopus
  • Page Numbers: pp.1025-1032

Abstract

Background Different diagnostic and classification criteria are available for hereditary recurrent fevers (HRF)-familial Mediterranean fever (FMF), tumour necrosis factor receptor-associated periodic fever syndrome (TRAPS), mevalonate kinase deficiency (MKD) and cryopyrin-associated periodic syndromes (CAPS)-and for the non-hereditary, periodic fever, aphthosis, pharyngitis and adenitis (PFAPA). We aimed to develop and validate new evidence-based classification criteria for HRF/PFAPA.