Classification criteria for autoinflammatory recurrent fevers


GATTORNO M., Hofer M., FEDERICI S., VANONI F., BOVIS F., AKSENTIJEVICH I., ...More

ANNALS OF THE RHEUMATIC DISEASES, vol.78, no.8, pp.1025-1032, 2019 (SCI-Expanded) identifier identifier identifier

Abstract

Background Different diagnostic and classification criteria are available for hereditary recurrent fevers (HRF)-familial Mediterranean fever (FMF), tumour necrosis factor receptor-associated periodic fever syndrome (TRAPS), mevalonate kinase deficiency (MKD) and cryopyrin-associated periodic syndromes (CAPS)-and for the non-hereditary, periodic fever, aphthosis, pharyngitis and adenitis (PFAPA). We aimed to develop and validate new evidence-based classification criteria for HRF/PFAPA.