Long-termoutcomes of six patients after partial internal biliary diversion for progressive familial intrahepatic cholestasis

Erginel, BAŞAK; Soysal, Feryal; Durmaz, ÖZLEM; Celik, Alaattin; Salman, Tansu

doi:10.1016/j.jpedsurg.2017.10.055

Long-termoutcomes of six patients after partial internal biliary diversion for progressive familial intrahepatic cholestasis

Erginel B., Soysal F. G., Durmaz O., Celik A., Salman T.

JOURNAL OF PEDIATRIC SURGERY, vol.53, no.3, pp.468-471, 2018 (SCI-Expanded, Scopus)

Publication Type: Article / Article
Volume: 53 Issue: 3
Publication Date: 2018
Doi Number: 10.1016/j.jpedsurg.2017.10.055
Journal Name: JOURNAL OF PEDIATRIC SURGERY
Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
Page Numbers: pp.468-471
Istanbul University Affiliated: Yes

Abstract

Background: Partial internal biliary diversion (PIBD) is an alternative approach for the treatment of devastating pruritus in patients with progressive familial intrahepatic cholestasis (PFIC). In these patients quality of life can be improved and progression of liver disease can be delayed while waiting for liver transplantation. The aim of our study was to evaluate six patients with PFIC who have undergone PIBD in long-term follow-up.