Long-termoutcomes of six patients after partial internal biliary diversion for progressive familial intrahepatic cholestasis

Erginel B., Soysal F. G., Durmaz O., Celik A., Salman T.

JOURNAL OF PEDIATRIC SURGERY, cilt.53, sa.3, ss.468-471, 2018 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 53 Sayı: 3
  • Basım Tarihi: 2018
  • Doi Numarası: 10.1016/j.jpedsurg.2017.10.055
  • Dergi Adı: JOURNAL OF PEDIATRIC SURGERY
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.468-471
  • İstanbul Üniversitesi Adresli: Evet

Özet

Background: Partial internal biliary diversion (PIBD) is an alternative approach for the treatment of devastating pruritus in patients with progressive familial intrahepatic cholestasis (PFIC). In these patients quality of life can be improved and progression of liver disease can be delayed while waiting for liver transplantation. The aim of our study was to evaluate six patients with PFIC who have undergone PIBD in long-term follow-up.