OHVIRA syndrome presenting with acute abdomen: a case report and review of the literature

Ugurlucan F., Bastu E., GULSEN G., Eken M. K., Akhan S. E.

CLINICAL IMAGING, cilt.38, sa.3, ss.357-359, 2014 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Derleme
  • Cilt numarası: 38 Sayı: 3
  • Basım Tarihi: 2014
  • Doi Numarası: 10.1016/j.clinimag.2013.12.011
  • Dergi Adı: CLINICAL IMAGING
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.357-359
  • İstanbul Üniversitesi Adresli: Evet

Özet

Uterus didelphys with obstructed hemivagina and ipsilateral renal agenesis (OHVIRA) or Herlyn-Werner-Wunderlich (HWW) syndrome is a rare congenital urogenital anomaly. A 13-year-old female presented with acute abdominal pain and dysmenorrhea. Ultrasonography and magnetic resonance imaging showed uterus didelphys, hematometrocolpos, obstructed hemivagina, and right renal agenesis. Hemivaginal septal resection and anastomosis between the obstructed hemivagina and the normal vagina was tried, but it was not possible. Unilateral hysterectomy was performed. HWW syndrome may present with acute abdomen and is usually treated with vaginal septum resection and drainage of the hematometrocolpos. (C) 2014 Elsevier Inc. All rights reserved.