OHVIRA syndrome presenting with acute abdomen: a case report and review of the literature

Ugurlucan F., Bastu E., GULSEN G., Eken M. K., Akhan S. E.

CLINICAL IMAGING, vol.38, no.3, pp.357-359, 2014 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Review
  • Volume: 38 Issue: 3
  • Publication Date: 2014
  • Doi Number: 10.1016/j.clinimag.2013.12.011
  • Journal Name: CLINICAL IMAGING
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.357-359
  • Istanbul University Affiliated: Yes


Uterus didelphys with obstructed hemivagina and ipsilateral renal agenesis (OHVIRA) or Herlyn-Werner-Wunderlich (HWW) syndrome is a rare congenital urogenital anomaly. A 13-year-old female presented with acute abdominal pain and dysmenorrhea. Ultrasonography and magnetic resonance imaging showed uterus didelphys, hematometrocolpos, obstructed hemivagina, and right renal agenesis. Hemivaginal septal resection and anastomosis between the obstructed hemivagina and the normal vagina was tried, but it was not possible. Unilateral hysterectomy was performed. HWW syndrome may present with acute abdomen and is usually treated with vaginal septum resection and drainage of the hematometrocolpos. (C) 2014 Elsevier Inc. All rights reserved.