Pulmonary atresia and ventricular septal defect with MAPCAs associated with right sided endocarditis and paradoxical embolic event


Oezden K., Mutlu B., Kahveci G., Bayrak F., Saltik L., Gueran S., ...Daha Fazla

EUROPEAN JOURNAL OF ECHOCARDIOGRAPHY, cilt.8, sa.4, ss.292-295, 2007 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 8 Sayı: 4
  • Basım Tarihi: 2007
  • Doi Numarası: 10.1016/j.euje.2006.03.004
  • Dergi Adı: EUROPEAN JOURNAL OF ECHOCARDIOGRAPHY
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.292-295
  • İstanbul Üniversitesi Adresli: Evet

Özet

Pulmonary atresia and ventricular septal defect (PA-VSD) with major aortopulmonary collaterals (MAPCAs) is a complex and extremely heterogeneous anomaly. PA-VSD with both pulmonary arteries originating from systemic arterial circulation without MAPCAs and patent ductus arteriosus (PDA) is a very rare disease and according to our knowledge a case without cyanosis and symptoms of congestive heart failure after the first decade of life has not been reported. The majority of untreated patients die in their first decade of life as a result of intractable congestive heart failure or respiratory distress. This report informs about a 21-year-old PA-VSD patient who presented without cyanosis with both pulmonary arteries arising from aorta associated with right sided endocarditis and a paradoxical embolic event. (C) 2006 The European Society of Cardiology. Published by Elsevier Ltd. All rights reserved.