Circumcision in a combined factor V and factor VIII deficiency using desmopressin (DDAVP)

DEVECIOGLU O., ERYILMAZ E., CELIK D., UNUVAR A., Karakas Z., ANAK S. S., ...Daha Fazla

TURKISH JOURNAL OF PEDIATRICS, cilt.44, sa.2, ss.146-147, 2002 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 44 Sayı: 2
  • Basım Tarihi: 2002
  • Dergi Adı: TURKISH JOURNAL OF PEDIATRICS
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.146-147
  • Anahtar Kelimeler: combined factor V and VIII deficiency, desmopression, circumcision
  • İstanbul Üniversitesi Adresli: Evet

Özet

Combined factor V and VIII deficiency is a rare inherited autosomal recessive single gene disorder commonly seen in the Middle East. Although the factor levels are between 5-30%, several authors have reported that these patients are more prone to bleeding compared to those having an isolated factor deficiency with the same levels. We report an eight-year-old boy with factor V and VIII deficiency who underwent a successful circumcision using desmopressin (DDAVP).