Circumcision in a combined factor V and factor VIII deficiency using desmopressin (DDAVP)


DEVECIOGLU O. , ERYILMAZ E., CELIK D., UNUVAR A., Karakas Z. , ANAK S. S. , ...More

TURKISH JOURNAL OF PEDIATRICS, vol.44, no.2, pp.146-147, 2002 (Journal Indexed in SCI) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 44 Issue: 2
  • Publication Date: 2002
  • Title of Journal : TURKISH JOURNAL OF PEDIATRICS
  • Page Numbers: pp.146-147

Abstract

Combined factor V and VIII deficiency is a rare inherited autosomal recessive single gene disorder commonly seen in the Middle East. Although the factor levels are between 5-30%, several authors have reported that these patients are more prone to bleeding compared to those having an isolated factor deficiency with the same levels. We report an eight-year-old boy with factor V and VIII deficiency who underwent a successful circumcision using desmopressin (DDAVP).