Circumcision in a combined factor V and factor VIII deficiency using desmopressin (DDAVP)

DEVECIOGLU O., ERYILMAZ E., CELIK D., UNUVAR A., Karakas Z., ANAK S. S., ...More

TURKISH JOURNAL OF PEDIATRICS, vol.44, no.2, pp.146-147, 2002 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 44 Issue: 2
  • Publication Date: 2002
  • Journal Name: TURKISH JOURNAL OF PEDIATRICS
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.146-147
  • Keywords: combined factor V and VIII deficiency, desmopression, circumcision
  • Istanbul University Affiliated: Yes

Abstract

Combined factor V and VIII deficiency is a rare inherited autosomal recessive single gene disorder commonly seen in the Middle East. Although the factor levels are between 5-30%, several authors have reported that these patients are more prone to bleeding compared to those having an isolated factor deficiency with the same levels. We report an eight-year-old boy with factor V and VIII deficiency who underwent a successful circumcision using desmopressin (DDAVP).