Atıf İçin Kopyala
Tugcu D., Salcıoglu Z., Akçay A., Sen H. S., Aydoğan G., Akıcı F., ...Daha Fazla
BLOOD COAGULATION & FIBRINOLYSIS, cilt.26, ss.145-151, 2015 (SCI-Expanded)
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Yayın Türü:
Makale / Tam Makale
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Cilt numarası:
26
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Basım Tarihi:
2015
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Doi Numarası:
10.1097/mbc.0000000000000204
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Dergi Adı:
BLOOD COAGULATION & FIBRINOLYSIS
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Derginin Tarandığı İndeksler:
Science Citation Index Expanded (SCI-EXPANDED), Scopus
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Sayfa Sayıları:
ss.145-151
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Anahtar Kelimeler:
childhood, clinical findings, prophylaxis, rare factor deficiency, severe bleeding, FACTOR-VII DEFICIENCY, COAGULATION DISORDERS, BLEEDING DISORDERS, PROPHYLAXIS, REGISTRY
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İstanbul Üniversitesi Adresli:
Evet
Özet
Background Rare factor deficiencies (RFDs) are autosomal recessively inherited coagulation factor deficiencies encountered at a frequency of between one in 500 000 and one in two million.