Auditory rehabilitation in neurofibromatosis type 2: a case for cochlear implantation.

Temple R., Axon P., Ramsden R., Keles N. , Deger K., Yucel E.

The Journal of laryngology and otology, vol.113, no.2, pp.161-3, 1999 (Journal Indexed in SCI Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 113 Issue: 2
  • Publication Date: 1999
  • Doi Number: 10.1017/s0022215100143452
  • Title of Journal : The Journal of laryngology and otology
  • Page Numbers: pp.161-3


Cochlear implantation has a limited but definite role in the rehabilitation of certain neurofibromatosis type 2 (NF2) patients. The presence of a dead ear either before, or after, tumour removal does not necessarily imply loss of function in the eighth nerve; in some instances the hearing loss will be cochlear. Promontory or round window electrical stimulation may help to identify those individuals with surviving eighth nerve function. In such patients multichannel cochlear implantation promises a better level of audition than the auditory brain stem implant. This paper highlights such a case and the management problems are discussed.