Kimura disease (KD) is a chronic inflammatory disorder with unknown etiology, most commonly manifesting as painless unilateral cervical lymphadenopathy or subcutaneous masses in the head or neck region. Kimura disease is in unusual vascular tumor that typically occurs at 20 to 30 years of age, more commonly in women. there has been no documented case of malignant transformation; however, recurrence rates after excision may be as high as 25%. Surgery and medical therapy are useful for treatment. We present a 28-year-old man developed a unilateral cervical mass associated with KID. We made a complete excisional resection of the mass. We Could not see any evidence of relapsing,and decided that proper surgical resection of the lesion can be a treatment for KD. Because the disease can be seen with nephritic syndrome and has different treatment options, the otolaryngology specialist Should consider KID in patients with neck mass and cosinophilia.