Combined valve and coronary surgery in a patient with erythropoietic protoporphyria

Akinci, E; Erentug, V; Bozbuga, NİLGÜN; Polat, A; Mansuroglu, D; Yakut, C

doi:10.1111/j.1540-8191.2005.200438.x

Combined valve and coronary surgery in a patient with erythropoietic protoporphyria

Akinci E., Erentug V., Bozbuga N., Polat A., Mansuroglu D., Yakut C.

JOURNAL OF CARDIAC SURGERY, vol.20, no.3, pp.267-268, 2005 (SCI-Expanded, Scopus)

Publication Type: Article / Article
Volume: 20 Issue: 3
Publication Date: 2005
Doi Number: 10.1111/j.1540-8191.2005.200438.x
Journal Name: JOURNAL OF CARDIAC SURGERY
Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
Page Numbers: pp.267-268
Istanbul University Affiliated: Yes

Abstract

Erythropoietic protoporphyria (EPP) is an autosomal dominant disorder of heme synthesis, causing excess of protoporphyrin in blood, skin, liver, and other organs. A 58-year-old male patient with EPP underwent aortic valve replacement and a concomitant aortocoronary bypass. The patient has been followed without complications due to EPP postoperatively. Cardiac surgery can safely be performed on patients with EPP by considering close attention not to stimulate porphyrin synthesis.