Combined valve and coronary surgery in a patient with erythropoietic protoporphyria

Akinci E., Erentug V., Bozbuga N., Polat A., Mansuroglu D., Yakut C.

JOURNAL OF CARDIAC SURGERY, cilt.20, sa.3, ss.267-268, 2005 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 20 Sayı: 3
  • Basım Tarihi: 2005
  • Doi Numarası: 10.1111/j.1540-8191.2005.200438.x
  • Dergi Adı: JOURNAL OF CARDIAC SURGERY
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.267-268
  • İstanbul Üniversitesi Adresli: Evet

Özet

Erythropoietic protoporphyria (EPP) is an autosomal dominant disorder of heme synthesis, causing excess of protoporphyrin in blood, skin, liver, and other organs. A 58-year-old male patient with EPP underwent aortic valve replacement and a concomitant aortocoronary bypass. The patient has been followed without complications due to EPP postoperatively. Cardiac surgery can safely be performed on patients with EPP by considering close attention not to stimulate porphyrin synthesis.