Progressive Pseudorheumatoid Dysplasia Misdiagnosed as Seronegative Juvenile Idiopathic Arthritis
ETHIOPIAN JOURNAL OF HEALTH SCIENCES, vol.26, no.4, pp.397-400, 2016 (ESCI, Scopus)
- Publication Type: Article / Article
- Volume: 26 Issue: 4
- Publication Date: 2016
- Doi Number: 10.4314/ejhs.v26i4.12
- Journal Name: ETHIOPIAN JOURNAL OF HEALTH SCIENCES
- Journal Indexes: Emerging Sources Citation Index (ESCI), Scopus
- Page Numbers: pp.397-400
- Istanbul University Affiliated: Yes
Abstract
BACKGROUND: Progressive pseudorheumatoid dysplasia (PPD) is a rare spondylo-epi-metaphyseal dysplasia (SEMD). It can be confused with juvenile idiopathic arthritis (JIA), both clinically and radiologically. Early detection and diagnosis of PPD are important in helping to relieve the pain and disability associated with this disease and in avoiding unnecessary investigations and anti-rheumatic interventions.