HEREDITARY HEMORHAGIC TELANGIECTASIA: A RARE CAUSE OF HEPATIC ENCEPHALOPATHY DUE TO PORTOSYSTEMIC SHUNT

Akpinar T. S., Kose M., Iliaz R., Evirgan S., Bulakci M., Yilmaz E., ...Daha Fazla

NOBEL MEDICUS, cilt.11, sa.3, ss.74-76, 2015 (ESCI) identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 11 Sayı: 3
  • Basım Tarihi: 2015
  • Dergi Adı: NOBEL MEDICUS
  • Derginin Tarandığı İndeksler: Emerging Sources Citation Index (ESCI), Scopus
  • Sayfa Sayıları: ss.74-76
  • Anahtar Kelimeler: Portosystemic shunt, hepatic encephalopathy, hereditary hemorrhagic telangiectasia, HEMORRHAGIC TELANGIECTASIA, INVOLVEMENT, DIAGNOSIS
  • İstanbul Üniversitesi Adresli: Evet

Özet

Hepatic encephalopathy is a common complication of end-stage liver disease. It happens in the presence of significant hepatic dysfunction and the diversion of the portal blood to the systemic circulation (porto-systemic shunts). Hereditary Hemorrhagic Telangiectasia (HHT) or Osler-Weber-Rendu disease, can also involve the liver along with the skin, mucous membranes, lung, brain, and gastrointestinal tract. The prevalence of hepatic involvement in HHT ranges between 41% and 78%. Although most patients with HHT are asymptomatic, some may have symptoms due to high-output heart failure, portal hypertension and biliary disease. Less commonly, patients may also develop porto-systemic encephalopathy. In this case report, we present a woman aged 63 years, who was diagnosed as having hepatic encephalopathy due to a portosystemic shunt.