Orbital muscle involvement in a child with familial Mediterranean fever


Keskindemirci G., Aktay Ayaz N., Cakan M., Er A., Bayramoglu S. E., Genc H. S.

MARMARA MEDICAL JOURNAL, cilt.29, ss.124-126, 2016 (ESCI) identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 29
  • Basım Tarihi: 2016
  • Doi Numarası: 10.5472/mmjcr.2902.05
  • Dergi Adı: MARMARA MEDICAL JOURNAL
  • Derginin Tarandığı İndeksler: Emerging Sources Citation Index (ESCI), Scopus, TR DİZİN (ULAKBİM)
  • Sayfa Sayıları: ss.124-126
  • Anahtar Kelimeler: Familial Mediterranean fever, Eye involvement, Orbital myositis
  • İstanbul Üniversitesi Adresli: Hayır

Özet

Familial Mediterranean fever is an autosomal recessively inherited autoinflammatory disorder characterized by recurrent attacks of fever, serositis and synovitis. Various atypical presentations have been reported in the literature. Herein, we report a case of orbital myositis presenting with acute and devastating ocular symptoms resembling orbital cellulitis in a 12-year-old boy with familial Mediterranean fever.