Anesthetic management of scoliosis operation in a pediatric patient with Frank-ter Haar syndrome: a case report

Basaran I., Gozubuyuk E., Canbolat N., Edipoglu I. S., Buget M.

BRAZILIAN JOURNAL OF ANESTHESIOLOGY, vol.71, no.2, pp.181-183, 2021 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 71 Issue: 2
  • Publication Date: 2021
  • Doi Number: 10.1016/j.bjane.2020.11.005
  • Journal Name: BRAZILIAN JOURNAL OF ANESTHESIOLOGY
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus, Directory of Open Access Journals
  • Page Numbers: pp.181-183
  • Keywords: Frank-ter Haar syndrome, Airway management, General anesthesia, Scoliosis
  • Istanbul University Affiliated: Yes

Abstract

Frank-ter Haar syndrome is a rare disorder characterized by multiple skeletal, cardiovascular abnormalities, and facial features. Some of these characteristic facial features are important for anesthesiologists to predict the difficult airway. We present the anesthesia management of an 8-year-old boy with Frank-ter Haar syndrome who underwent posterior spinal instrumentation operation for scoliosis. In these patients, it is vital to anticipate possible difficult intubation before surgery and make all necessary preparations. (C) 2021 Sociedade Brasileira de Anestesiologia. Published by Elsevier Editora Ltda.