IDIOPATHIC TOLOSA-HUNT SYNDROME: FOUR ADDITIONAL CASES

Kirbas D., Topcular B., Ozcan M. E., Sakalli K. N., Gul G., Aslan K.

IDEGGYOGYASZATI SZEMLE-CLINICAL NEUROSCIENCE, vol.61, pp.250-254, 2008 (SCI-Expanded)

  • Publication Type: Article / Article
  • Volume: 61
  • Publication Date: 2008
  • Journal Name: IDEGGYOGYASZATI SZEMLE-CLINICAL NEUROSCIENCE
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.250-254
  • Istanbul University Affiliated: No

Abstract

Idiopathic Tolosa Hunt syndrome (ITHS) is a very rare cause of painful ophthalmoplegia characterized by unilateral orbital pain, ipsilateral oculomotor paralysis and prompt response to steroids. In this paper we report 4 additional cases of ITHS. This rare cause of painful ophthalmoplegia effects the cranial nerves due to a granulomatous lesion of unknown etiology in the cavernous sinus or superior orbital fissure. The International Headache Society redefined the diagnostic criteria for ITHS but it is still mostly a diagnosis of exclusion. Careful evaluation and follow-up is essential for diagnosis. Optimal therapy duration and dosage and prophylactic treatment in recurrent cases needs further research.

Idiopathic Tolosa Hunt syndrome (ITHS) is a very rare cause of painful ophthalmoplegia characterized by unilateral orbital pain, ipsilateral oculomotor paralysis and prompt response to steroids. In this paper we report 4 additional cases of ITHS. This rare cause of painful ophthalmoplegia effects the cranial nerves due to a granulomatous lesion of unknown etiology in the cavernous sinus or superior orbital fissure. The International Headache Society redefined the diagnostic criteria for ITHS but it is still mostly a diagnosis of exclusion. Careful evaluation and follow-up is essential for diagnosis. Optimal therapy duration and dosage and prophylactic treatment in recurrent cases needs further research.